Progeria Cellular Mechanics LMNA / HGPS Sim

Honoring advocate Michiel Vandeweert & HGPS research

Nuclear Envelope Biomechanics

Lamin A Envelope
Toxic Progerin Accumulation
FTI Therapeutic Block
DNA Strain Points

Cellular Health Metrics

Membrane Blebbing
68%
Nuclear Integrity
32%
Senescence Rate
High
Longevity Gain
+0.0 yrs
Pathology Overview: A point mutation in LMNA (c.1824 C>T) creates a truncated lamin A variant called Progerin. Retaining a hydrophobic farnesyl group, it permanently anchors into the inner nuclear membrane, inducing stiffening, blebbing, and DNA damage.

HGPS Clinical Progression & Lifespan Counterfactual

Onset (9-24m)
Symptom Cascade
Untreated Median (14.5y)
FTI Extended (20y+)
Select a clinical milestone on the timeline above to inspect biomechanical onset, vascular smooth muscle degradation, and therapeutic target windows.
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